ACTA
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Table of Contents for Decembar 2021 • Volume 37 • Number 84 |
PARRY ROMBERG SYNDROME WITH EN COUP DE SABRE: A REPORT OF A RARE CASE
Mohamed Faizal Asan1,
1NITTE
(DEEMED TO BE UNIVERSITY), AB SHETTY MEMORIAL INSTITUTE
OF DENTAL SCIENCES, DEPARTMENT OF ORAL MEDICINE AND
RADIOLOGY MANGALORE, INDIA
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...Abstract |
The basis of the
problem: Parry Romberg syndrome (PRS) is a rare developmental
disorder manifesting as a slow and progressive atrophy of the face which
is often unilateral, hence also termed as rpogressivehemifacial atrophy.
The extent of the atrophy may vary, involving the superficial skin
extending upto the underlying bone. The clinical features of PRS include
craniofacial, neurologic, ophthalmic and dermatological manifestations,
which result in various functional and psychological problems. PRS and
linear scleroderma belong to the same disease spectrum. There can be
demarcating line between the normal and abnormal skin seen in PRS,
termed as “en coup de sabre”. PRS is most commonly seen in females and
involves the left side of the face. Key words: cone-beam computed tomography, hemifacial atrophy, maxillofacial abnormalities, rare diseases.
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...Authors and Reprint Information |
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